Retinal changes in sickle cell/hereditary persistence of fetal haemoglobin syndrome.
نویسندگان
چکیده
We describe for the first time retinal changes in sickle cell/hereditary persistence of fetal haemoglobin syndrome, which is a rare and benign disorder. The changes are qualitatively similar to retinal disease seen with sickle haemoglobin and sickle C haemoglobin, but are mild.
منابع مشابه
Ocular findings in children with sickle cell haemoglobin C disease in Jamaica.
The development of severe retinal vascular disease and retinitis proliferans in sickle cell haemoglobin C disease (SC disease) is well recognized (Welch and Goldberg, I966; Goldberg, 197I; Condon and Serjeant, I972a). In a recent survey in Jamaica, Condon and Serjeant (1972a) noted retinitis proliferans in 23 (33 per cent.) of seventy adults with SC disease. The changes were found in some patie...
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عنوان ژورنال:
- The British journal of ophthalmology
دوره 67 11 شماره
صفحات -
تاریخ انتشار 1983